Pulmonary Assessment and Management of Patients with Pediatric Neuromuscular Disease

Description:



Pulmonary Assessment and Management of Patients with Pediatric Neuromuscular Disease covers the broad medical problems and specific pulmonary conditions in patients with pediatric neuromuscular disease, ranging from the different types of neuromuscular disease, their pathophysiology, and assessment and management, including both novel disease modifying pharmacotherapies and state-of-the-art clinical management. This book provides evidence-based guidance for pediatric patients with neuromuscular disease, and is a valuable resource to pediatric pulmonologists, critical care physicians, and respiratory therapists who want an update and understanding on the cutting-edge therapies and standards of care for managing this population.

Features:

• Provides a single comprehensive source of information to properly guide pulmonary assessments of pediatric neuromuscular disease
• Discusses recent advancements in both medications and clinical respiratory management for pediatric patients
• Covers different types of neuromuscular disease, including spinal muscular atrophy, Duchenne muscular dystrophy, congenital muscular dystrophy, and more

Table Of Contents:

Section 1: Introduction

1. Types of neuromuscular disease

2. Pulmonary pathophysiology of neuromuscular disease

3. Natural history

Section 2: Assessment

4. Assessment of pulmonary function

5. Assessment of hypoventilation

6. Assessment of need for airway clearance

Section 3: Clinical Management

7. Pharmacotherapies

8. Airway clearance

9. Aerodigestive Problems and Management

10. Chronic mechanical ventilation

11. Thoracospinal disease

12. Challenges in managing hypertonic neuromuscular disease

13. Acute management

14. Home management

Section 4: Patient focused

15. Transition from pediatric to adult care

Section 5: Conclusion

16. Changing natural history